Tumor neuroectodérmico primitivo: A propósito de um caso clínico
DOI:
https://doi.org/10.34631/sporl.272Palavras-chave:
PNET, tumor neuroectodérmico primitivo, sarcoma de Ewing/PNET, PNET periféricoResumo
Os tumores neuroectodérmicos primitivos (PNET) são um grupo de tumores com um comportamento muito agressivo que raramente se apresentam na região da cabeça e pescoço. Um dos factores de prognóstico mais significativo é a presença ou ausência de metástases.
O tratamento deve ser agressivo, mas o uso de quimioterapia permitiu melhorar a sobrevida a longo prazo dos doentes com este tipo de tumor. Os autores descrevem o caso clínico de um doente com um tumor neuroectodérmico periférico (Grupo Ewing/ PNET) localizado na nasofaringe com extensão aos seios peri-nasais.
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