Incus long process dysplasia – a clinical case
DOI:
https://doi.org/10.34631/sporl.3133Keywords:
Dysplasia, Incus, MalformationAbstract
Middle ear malformations are rare events, occurring in approximately 1 in 15,000 live births.1–3 They are generally associated with other head and neck anomalies and may also be part of syndromic malformations. Isolated malformations of the middle ear are therefore even rarer and pose a diagnostic challenge4, especially given the normal appearance of the auricle, external auditory canal, and tympanic membrane.
In this article, we describe the clinical case of a 19-year-old female patient with a history of untreated hearing loss since childhood. Otolaryngological examination revealed no abnormalities, prompting further audiometric evaluation. Pure tone audiometry demonstrated a left-sided conductive hearing loss with an air-bone gap (ABG) of 54 dB and a type A tympanogram. Computed tomography (CT) was reported as normal. An exploratory tympanotomy was therefore performed, revealing an isolated dysplasia of the long process of the incus. A type II ossiculoplasty (Portmann classification)14 was performed using autologous cortical mastoid bone and tragal cartilage grafts. The postoperative audiogram showed a reduction in the average ABG to 18.75 dB.
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Copyright (c) 2025 António Trigueiros Cunha, Nuno Trigueiros Cunha, Constança Oom Duarte, João Rainha Fernandes, Maria Pimenta Machado, Carlos Macor
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