Angiocentric Eosinophilic Fibrosis: Case Report

Authors

  • Thais Potter Cardeira Pedro Faculdade de Medicina de Jundiaí, Brasil
  • Lucas Ferreira Siqueira Faculdade de Medicina de Jundiaí, Brasil
  • Vivane Cristina Martori Pandini Faculdade de Medicina de Jundiaí, Brasil
  • Edmir Américo Lourenço Faculdade de Medicina de Jundiaí, Brasil

DOI:

https://doi.org/10.34631/sporl.938

Keywords:

Eosinophilic Angiocentric Fibrosis, nasal obstruction, fibrosis, nasal cavity

Abstract

Angiocentric Eosinophilic Fibrosis is a rare disease, that affects the nasal cavity and upper respiratory tract. Its etiology is still not yet clarified, and symptoms consist in obstruction of the upper airways. Macroscopically, it presents as a pink-white lesion, varying in size and extension, with possible ulceration. It is currently a diagnosis of exclusion, and defined by imuno-histological aspects. Possible relation with IgG4-mediated diseases is being currently investigated. So far treatment is mainly surgical, with special attention regarding post-surgical recurrences of the disease.

References

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Published

2021-12-17

How to Cite

Potter Cardeira Pedro, T., Siqueira, L. F., Martori Pandini, V. C. ., & Lourenço, E. A. (2021). Angiocentric Eosinophilic Fibrosis: Case Report. Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery, 59(4), 397–401. https://doi.org/10.34631/sporl.938

Issue

Vol. 59 No. 4 (2021): December

Section

Case Report

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Copyright (c) 2021 Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery

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