Cochlear aplasia as an imagiological finding
DOI:
https://doi.org/10.34631/sporl.461Keywords:
congenital hearing loss, cochlear aplasiaAbstract
The authors present a clinical case of congenital hearing loss due to cochlear aplasia diagnosed at 58 years old, as a imagiological finding during the study of a chronic otitis media. Cochlear aplasia is a rare congenital malformation that represents only 3% of cochlear malformations. It is characterized by the complete absence of the cochlea, with the presence of remnants of the vestibule and semicircular canals. It is to emphasize the importance of attentive taking of medical history, suspicion and investigation of the cause of deafness, even when this can be explained by another recognized condition.
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