Epistaxis as first manifestation of Wegener's granulomatosis. Clinical case
DOI:
https://doi.org/10.34631/sporl.271Keywords:
epistaxis, Wegener's Granulomatosis, vasculitis, granulomaAbstract
Wegener's granulomatosis is a systemic disease of unknown ethiology, characterized by a clinical triad of paranasal sinus and nasal mucosa involvement, pulmonary infiltration and cavitation, and renal disease with hematuria. Wegener's granulomatosis usually affects young or middle-aged adults. Although is uncommon in children, patients can be affected at any age.
We describe a clinical case of a 14-year-old girl presentation with epistaxis, subsequent investigation showed renal failure and multiple pulmonary nodules. A positive proteinase antineutrophilic cytoplasmic antibody test supported the diagnosis of Wegener's Granulomatosis, requiring dialysis and immunosupression.
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