Microtia and congenital atresia of the external auditory canal: a case report
DOI:
https://doi.org/10.34631/sporl.2172Keywords:
Microtia, Congenital atresia of the external auditory canal, Deafness, Osteointegrated hearing implantAbstract
Microtia and congenital atresia of the external auditory canal (EAC) are congenital malformations of the external ear that are often associated. Microtia results from a malformation of the auricle, while congenital atresia is a total or partial occlusion of the EAC. The challenge for the otolaryngologist is the management, which may include reconstructive surgery and auditory rehabilitation. Each case is unique and requires an individualized approach by a specialized team of otolaryngologists and plastic surgeons. We present the case of a 62-year-old woman with microtia and congenital atresia of the right EAC, with a history of reconstructive surgery of the pinna, in which auditory rehabilitation with an osseointegrated implant was chosen.
References
Bartel-Friedrich S, Wulke C. Classification and diagnosis of ear malformations. GMS Curr Top Otorhinolaryngol Head Neck Surg. 2007:6:Doc05.
Campo AA, Victor-Baldin A, Contreras-Mérida SM. Surgical-based classification for microtia. J Craniofac Surg. 2018 Sep;29(6):1651-1654. doi: 10.1097/SCS.0000000000004772.
Zhang TY, Bulstrode N, Chang KW, Cho YS, Frenzel H, Jiang D. et al. International consensus recommendations on microtia, aural atresia and functional ear reconstruction. J Int Adv Otol. 2019 Aug;15(2):204-208. doi: 10.5152/iao.2019.7383.
Shonka DC Jr, Livingston WJ 3rd, Kesser BW. The Jahrsdoerfer grading scale in surgery to repair congenital aural atresia. Arch Otolaryngol Head Neck Surg. 2008 Aug;134(8):873-7. doi: 10.1001/archotol.134.8.873.
Watkinson JC, Clarke R. editors. Scott-Brown’s Otorhinolaryngology Head and Neck Surgery, Volume 2: Paediatrics, The Ear, and Skull Base Surgery. Boca Raton: CRC Press; 2018.
Abdel-Aziz M. Congenital aural atresia. J Craniofac Surg. 2013 Jul;24(4):e418-22. doi: 10.1097/SCS.0b013e3182942d11.
van Hövell Tot Westerflier CVA, van Heteren JAA, Breugem CC, Smit AL, Stegeman I. Impact of unilateral congenital aural atresia on academic performance: a systematic review. Int J Pediatr Otorhinolaryngol. 2018 Nov:114:175-179. doi: 10.1016/j.ijporl.2018.09.002.
Chang SO, Min YG, Kim CS, Koh TY. Surgical management of congenital aural atresia. Laryngoscope. 1994 May;104(5 Pt 1):606-11. doi: 10.1002/lary.5541040514.
Vázquez de la Iglesia F, Cervera-Paz FJ, Manrique Rodríguez M. Surgery for Atresia auris. Retrospective study of our results and correlation with Jahrsdoerfer prognostic criterium. Acta Otorrinolaringol Esp. 2004 Aug-Sep;55(7):315-9. doi: 10.1016/s0001-6519(04)78529-5.
Seong J, Yang SK, Jang P, Lee SY, Carandang M, Choi BY. Clinical factors influencing the trial and purchase of bilateral microphones with contralateral routing of signal in patients with asymmetric sensorineural hearing loss. J Audiol Otol. 2020 Jan;24(1):29-34. doi: 10.7874/jao.2019.00409.
Hagr A. BAHA: bone-anchored hearing aid. Int J Health Sci (Qassim). 2007 Jul;1(2):265-76.
Baguley DM, Bird J, Humphriss RL, Prevost AT. The evidence base for the application of contralateral bone anchored hearing aids in acquired unilateral sensorineural hearing loss in adults. Clin Otolaryngol. 2006 Feb;31(1):6-14. doi: 10.1111/j.1749-4486.2006.01137.x.
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2024 Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery
This work is licensed under a Creative Commons Attribution-ShareAlike 4.0 International License.
