When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report

Authors

DOI:

https://doi.org/10.34631/sporl.997

Keywords:

Langerhans cell Histiocytosis, Pre-septal cellulitis, Frontal bone, Orbit, Pediatrics

Abstract

Langerhans cell histiocytosis (LCH) is a rare and heterogeneous disease that appears mainly in children and frequently affects bone structures such as the skull, with possible involvement of the orbit. In this paper, we present the case of an 11-year-old boy who came to the emergency department with left periorbital edema and erythema with about 10 days of progressive worsening. Computed tomography was compatible with complicated left frontal sinusitis with bone erosion into the orbit and intracranial compartment, and magnetic resonance imaging corroborated these findings. Due to the lack of improvement with medical therapy, surgical exploration was performed through an external approach, identifying a lesion in which the anatomopathological study confirmed the diagnosis of LCH.

References

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Published

2022-03-30

How to Cite

Teixeira, H., Lopes, M. B., Pedro, R. S., Rosa, M. H., & Antunes, L. (2022). When it’s not a complicated frontal sinusitis - A Langerhans Cell Histiocytosis case-report. Portuguese Journal of Otorhinolaryngology and Head and Neck Surgery, 60(1), 69–71. https://doi.org/10.34631/sporl.997

Issue

Section

Case Report