Biphenotypic Sinonasal Sarcoma: Case Report
DOI:
https://doi.org/10.34631/sporl.988Keywords:
Biphenotypic Sinonasal Sarcoma, Ethmoid Tumor, Sarcoma, Sinonasal NeoplasmAbstract
Biphenotypic Sinonasal Sarcoma (BSS) is a rare tumor, exclusive to the sinonasal tract, described relatively recently and which is known for its peculiar features. It is a low-grade malignant sarcoma, with cells showing features of neural and myogenic differentiation, which tends to recur locally and does not metastasize. We present the case of a 36-year-old man who presented nasal respiratory insufficiency due to a unilateral mass. After surgery, a low-grade mesenchymal tumor was diagnosed. During follow-up, after 6 years, a 3-cm sphenoid tumor was detected, which after excision was confirmed as biphenotypic sinonasal sarcoma.
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