Fibrose quística: Relação entre rinossinusite crónica e doença pulmonar
DOI:
https://doi.org/10.34631/sporl.888Palavras-chave:
Fibrose Quística, Rinossinusite CrónicaResumo
Objetivos: Avaliar a relação entre a Rinossinusite Crónica (RSC) e a Doença Pulmonar (DP) nos doentes com Fibrose Quística (FQ).
Material e Métodos: Estudo retrospetivo de doentes com FQ observados entre Janeiro de 2010 e Dezembro de 2019 na Consulta de ORL. Analisados parâmetros das provas de função respiratória, tomografia computorizada do tórax, necessidade de transplante pulmonar, colonização pulmonar e internamentos por agudização da doença respiratória e avaliada a sua associação com a presença e gravidade de RSC.
Resultados: Analisaram-se 44 doentes com idade média de 14.7 ±1.23 anos. 59.1% apresentavam RSC, com um score de Lund-Mackay médio de 8.38 (±6.4). A presença de RSC associou-se a maior necessidade de transplantação pulmonar (p=0.04), sendo que estes doentes apresentavam um score de Lund-Mackay mais elevado (14.9±5.8 vs. 7.8±5.1, p=0.012). A RSC não influenciou os resultados das provas de função respiratória.
Conclusões: A RSC pode influenciar a evolução da DP em doentes com FQ.
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