Epistaxis as first manifestation of acute adult idiopathic thrombocytopenic purpura. Clinical case

Autores

  • António Gómez-Torres Unidad de Gestión Clínica de Otorrinolaringología, Hospital Universitario Virgen del Rocío, Sevilla, España
  • Alicia Menoyo Bueno Unidad de Gestión Clínica de Otorrinolaringología, Hospital Universitario Virgen del Rocío, Sevilla, España
  • Ana Isabel Lorente Lavirgen Unidad de Gestión Clínica de Dermatología Médico-Quirúrgica y Venereología, Hospital Universitario Virgen del Rocío, Sevilla, España
  • António Abrante Jiménez Unidad de Gestión Clínica de Otorrinolaringología, Hospital Universitario Virgen del Rocío, Sevilla, España
  • Francisco Esteban Ortega Unidad de Gestión Clínica de Otorrinolaringología, Hospital Universitario Virgen del Rocío, Sevilla, España

DOI:

https://doi.org/10.34631/sporl.50

Palavras-chave:

epistaxis, systemic disease, idiopathic thrombocytopenic purpura

Resumo

Idiopathic thrombocytopenic purpura (ITP) is a common hematologic disorder characterized by immune-mediated platelet destruction; it is usually a benign, self-limiting disease in children. The disorder typically presents with purpura and petechiae after viral processes of the upper airway. We report a case of a young man who came to the Emergency department with a very severe epistaxis. After nasal package of the nose, a full blood count showed no platelets. Case series of epistaxis always refer to hematologic disorder and treatment but it is very rare to find epistaxis as the first sign of ITP. ITP was diagnosed and treatment for the disease was instituted with a favorable response.

Referências

- Monjas-Cánova I, Hernández-García I, Mauri-Barberá J, Sanz-Romero B, et al. Epidemiología de las epistaxis ingresadas en un hospital de tercer nivel. Acta Otorrinolaringol Esp. 2010;61:41–47.

- Pino Rivero V, Trinidad Ruiz G, González Palomino A, Pardo Romero G, et al. Consideraciones sobre las urgencias ORL. Análisis de 30.000 pacientes atendidos en 10 años. Acta Otorrinolaringol Esp. 2005;56:198-201.

- Moñux A, Tomás M, Kaiser C, Gavilan J. Conservative management of epistaxis. J Laryngol Otol. 1990;104:868–70.

- McCrac K. Immune thrombocytopenic: no longer “idiopathic”. Cleve Clin J Med 2011;78:358-73.

- Cines DB, McMillan R. Management of adult idiopathic thrombocytopenic purpura. Annu Rev Med 2005;56:425-42.

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Como Citar

Gómez-Torres, A., Bueno, A. M., Lavirgen, A. I. L., Jiménez, A. A., & Ortega, F. E. (2013). Epistaxis as first manifestation of acute adult idiopathic thrombocytopenic purpura. Clinical case. Revista Portuguesa De Otorrinolaringologia-Cirurgia De Cabeça E Pescoço, 51(4), 249–250. https://doi.org/10.34631/sporl.50

Edição

Secção

Caso Clínico